Developmental Trajectories for Spatial Frames of Reference in Williams Syndrome

Autor/inn/en	Nardini, Marko; Atkinson, Janette; Braddick, Oliver; Burgess, Neil
Titel	Developmental Trajectories for Spatial Frames of Reference in Williams Syndrome
Quelle	In: Developmental Science, 11 (2008) 4, S.583-595 (13 Seiten) PDF als Volltext Verfügbarkeit
Sprache	englisch
Dokumenttyp	gedruckt; online; Zeitschriftenaufsatz
ISSN	1363-755X
DOI	10.1111/j.1467-7687.2007.00662.x
Schlagwörter	Genetic Disorders; Developmental Stages; Child Development; Spatial Ability; Children; Adults; Visual Perception; Neurological Impairments; Cognitive Ability; Developmental Delays; Navigation; Inhibition; Cognitive Processes + Suchen Sie Ihr Suchwort? Kindesentwicklung; Räumliches Vorstellungsvermögen; Child; Kind; Kinder; Visuelle Wahrnehmung; Neurodegenerative Erkrankung; Denkfähigkeit; Entwicklungsverzögerung; Hemmung; Cognitive process; Kognitiver Prozess
Abstract	Williams syndrome (WS) is a genetic disorder associated with severe visuocognitive impairment. Individuals with WS also report difficulties with everyday wayfinding. To study the development of body-, environment-, and object-based spatial frames of reference in WS, we tested 45 children and adults with WS on a search task in which the participant and a spatial array are moved with respect to each other. Although individuals with WS showed a marked delay, like young controls they demonstrated independent, additive use of body- and environment-based frames of reference. Crucially, object-based (intrinsic) representations based on local landmarks within the array were only marginally used even by adults with WS, whereas in typical development these emerge at 5 years. Deficits in landmark use are consistent with wayfinding difficulties in WS, and may also contribute to problems with basic localization, since in typical development landmark-based representations supplement those based on the body and on self-motion. Difficulties with inhibition or mental rotation may be further components in the impaired ability to use the correct reference frame in WS. (As Provided).
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Erfasst von	ERIC (Education Resources Information Center), Washington, DC
Update	2017/4/10